Hyperammonemic encephalopathy in the ICU: two case reports.

Authors

  • L. Braconnier Service de réanimation polyvalente, CHU de Lille, université de Lille
  • A.J. Simonnet Service de réanimation polyvalente, CHU de Lille, université de Lille
  • M. Houard Service de réanimation polyvalente, CHU de Lille, université de Lille
  • Y. Benzidi Service de réanimation polyvalente, centre hospitalier Notre-Dame de la Miséricorde
  • L. Robriquet Service de réanimation polyvalente, CHU de Lille, université de Lille
  • C. Douillard Service d’endocrinologie et des maladies métaboliques, CHU de Lille, université de Lille
  • M. Jourdain Service de réanimation polyvalente, CHU de Lille, université de Lille

DOI:

https://doi.org/10.3166/rea-2018-0073

Keywords:

Hemophagocytic lymphohistiocytosis, Macrophage activation syndrome, Acute kidney injury

Abstract

We report the cases of 2 adult patients who were admitted in the intensive care unit for hyperammonemic coma. Metabolic blood tests revealed inborn urea cycle disorder in one case and a secondary hyperammonemic disorder in the other case. Urea cycle disorder may be diagnosed in the adulthood, and the late presentation does not exclude acute and life-threatening manifestations.

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Published

2018-12-13

How to Cite

Braconnier, L., Simonnet, A., Houard, M., Benzidi, Y., Robriquet, L., Douillard, C., & Jourdain, M. (2018). Hyperammonemic encephalopathy in the ICU: two case reports. Médecine Intensive Réanimation, 27(6), 558–562. https://doi.org/10.3166/rea-2018-0073

Issue

Vol. 27 No. 6 (2018): Novembre 2018 / Néphrologie et métabolisme

Section

Commented case report

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